Abstract
Introduction. ALCAPA is a congenital heart defect in which the left coronary artery arises from the pulmonary artery. Usually this is an isolated defect, but sometimes it can be associated with other cardiological defects. If left untreated, up to 90% of patients with this syndrome die within the first year of life. ALCAPA can be diagnosed with echocardiogram. This disease is treated surgically.
Case description. This is a clinical case of a 5-month-old girl who was diagnosed with anomalous left coronary artery from the pulmonary artery (ALCAPA). She also had left ventricle dilatation with reduced left ventricular ejection fraction and moderate mitral valve regurgitation.
She was born at 41 weeks gestation with a cesarean section. The neonatal period was normal. Girls development was good, she gained almost 1 kilogram every month. This patient was sent to a cardiology outpatient clinic by her family doctor, because of mild tachypnoea. At that time no other symptoms were noted. The diagnosis was confirmed by echocardiogram and diagnostic coronary angiography. Echocardiography showed left coronary artery anomaly, left ventricle dilatation with reduced left ventricular ejection fraction (28%), and moderate mitral valve regurgitation. Diagnostic coronary angiography showed an enlarged right coronary artery, that had a network of collateral flow. The patient received diuretics, aspirin, and beta blockers. In stable condition patient was
operated. She underwent surgical repair of ALCAPA from the pulmonary artery by direct implantation into the aorta. Her postoperative period was uneventful.
During the next 6 months after the operation left ventricle recovered without dilatation, with normal ejection fraction, but mild residual mitral and aortic valve insufficiencies remained.
Conclusion. This case demonstrates a rare and potentially fatal disease. Early detection of ALCAPA is important because surgery that is performed at the right time is associated with a positive outcome.
Case description. This is a clinical case of a 5-month-old girl who was diagnosed with anomalous left coronary artery from the pulmonary artery (ALCAPA). She also had left ventricle dilatation with reduced left ventricular ejection fraction and moderate mitral valve regurgitation.
She was born at 41 weeks gestation with a cesarean section. The neonatal period was normal. Girls development was good, she gained almost 1 kilogram every month. This patient was sent to a cardiology outpatient clinic by her family doctor, because of mild tachypnoea. At that time no other symptoms were noted. The diagnosis was confirmed by echocardiogram and diagnostic coronary angiography. Echocardiography showed left coronary artery anomaly, left ventricle dilatation with reduced left ventricular ejection fraction (28%), and moderate mitral valve regurgitation. Diagnostic coronary angiography showed an enlarged right coronary artery, that had a network of collateral flow. The patient received diuretics, aspirin, and beta blockers. In stable condition patient was
operated. She underwent surgical repair of ALCAPA from the pulmonary artery by direct implantation into the aorta. Her postoperative period was uneventful.
During the next 6 months after the operation left ventricle recovered without dilatation, with normal ejection fraction, but mild residual mitral and aortic valve insufficiencies remained.
Conclusion. This case demonstrates a rare and potentially fatal disease. Early detection of ALCAPA is important because surgery that is performed at the right time is associated with a positive outcome.
| Original language | English |
|---|---|
| Pages | 15 |
| Number of pages | 1 |
| Publication status | Published - 29 Apr 2023 |
| Externally published | Yes |
| Event | International Student Conference on Pediatrics 2023 - Online Duration: 29 Apr 2023 → 29 Apr 2023 https://www.facebook.com/events/933320701029347/?paipv=0&eav=AfaYeuQhKpeiAKKGnhqzCKDcADcPYBOyak2aPQTfE59gBKhSd-Iif5WK1q_ap72jdxY&_rdr |
Conference
| Conference | International Student Conference on Pediatrics 2023 |
|---|---|
| Period | 29/04/23 → 29/04/23 |
| Internet address |
Field of Science*
- 3.2 Clinical medicine
Publication Type*
- 3.4. Other publications in conference proceedings (including local)