Abstract
Eosinophilic granulomatosis with polyangiitis (EGPA; formerly known as Churg-Strauss syndrome) is classified as an antineutrophil cytoplasmic antibody (ANCA)-associated small vessel vasculitis. It is a multisystem disorder and can affect every organ system. EGPA is a rare disease, with an estimated prevalence of 1/70,000–100,000 in Europe. As its onset usually occurs in adulthood, data from pediatric patients are limited. We present here a very rare practical EGPA clinical case involving a pediatric patient. Presently, data on mepolizumab usage in pediatric patients are limited, with only a few case reports published.
Original language | English |
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Pages (from-to) | 973-979 |
Journal | Pediatric Pulmonology |
Volume | 58 |
Issue number | 3 |
DOIs | |
Publication status | Published - Mar 2023 |
Keywords*
- mepolizumab in pediatrics
- pediatric EGPA
- small vessel vasculitis
Field of Science*
- 3.2 Clinical medicine
Publication Type*
- 1.1. Scientific article indexed in Web of Science and/or Scopus database