One-step lower leg reconstruction with vascularized functional vastus lateralis muscle flap in the treatment of embryonal rhabdomyosarcoma for a six-month-old boy: A case report

Dzintars Ozols (Coresponding Author), Marisa Maija Berezovska, Janis Krasts, Marika Grutupa, Aigars Petersons

Research output: Contribution to journalArticlepeer-review

Abstract

Rhabdomyosarcoma (RMS) is a common soft tissue sarcoma in childhood, however, it is very rare in the neonatal period (0.4–2% of cases). This case depicts a boy, who presented with RMS at two weeks of age, but officially diagnosed at the age of three months. MRI and scintigraphy determined a soft tissue tumor in the soleus muscle, while biopsy confirmed embryonal RMS with high mitotic activity (Ki67 (monoclonal antibodies) ~80%). CWS (Cooperative Weichteilsarkom Studiengruppe)-2012 with I2VA (ifosfamide, vincristine, actinomycin) chemotherapy regimen was administered per protocol. Surgical treatment was performed at age of six months and 18 days. The operation consisted of radical tumor resection and total triceps surae with partial fibula resection. Immediate reconstruction of triceps muscle was accomplished using a vascularized functional musculocutaneous vastus lateralis flap. Functional outcome was measured using the Lower Extremity Functional Scale (LEFS) and the Foot and Ankle Outcome Score (FAOS) with the results of 92.5% and 99% respectively.

Original languageEnglish
Article number362
Pages (from-to)1-7
Number of pages7
JournalMedicina (Lithuania)
Volume56
Issue number7
DOIs
Publication statusPublished - 2020

Keywords

  • Embryonal rhabdomyosarcoma
  • Functional vastus transplantation
  • Infant microsurgery

Field of Science

  • 3.2 Clinical medicine

Publication Type

  • 1.1. Scientific article indexed in Web of Science and/or Scopus database

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