TY - JOUR
T1 - Palliative Care for Children and Adults With Inherited Metabolic Disease in Europe
T2 - An Underutilised Service for Supportive Treatment and Care
AU - Lee, Anja
AU - Bliksrud, Yngve Thomas
AU - Onali, Michela
AU - Neugebauer, Julia
AU - Eyskens, Francois
AU - Haas, Dorothea
AU - Mossler, Karin
AU - Enekwe, Antije
AU - Kiec-Wilk, Beata
AU - Diep, Lien My
AU - Bellettato, Cinzia Maria
AU - Zernikow, Boris
AU - Scarpa, Maurizio
AU - Rahman, Shamima
AU - Tangeraas, Trine
AU - MetabERN collaboration group on palliative care
AU - Lund, Allan M.
AU - Nassogne, Marie Cécile
A2 - Aarsand, Aasne K.
A2 - Aguiar, Patrício
A2 - Anaϊs, Brassier
A2 - Arnoux, Jean Baptiste
A2 - Auzenbaha, Madara
A2 - Azevedo, Olga
A2 - Bandeira, Anabela Oliveira
A2 - Belanger-Quintana, Amaya
A2 - Bellusci, Marcello
A2 - Belmatoug, Nadia
A2 - Bordugo, Andrea
A2 - Bosch, Annet M.
A2 - Botti, Mara
A2 - Brůha, Radan
A2 - Campos, Teresa
A2 - Cancelinha, Cândida
A2 - Ceccarini, Giovanni
A2 - Cefalo, Graziella
A2 - Cerkauskiene, Rimante
A2 - Crushell, Ellen
A2 - Chaves, Paulo Castro
A2 - Das, Anibh Martin
A2 - De Laet, Corinne
A2 - Derks, Terry G.J.
A2 - Distelmaier, Felix
A2 - Dobbelaere, Dries
A2 - Durães, João
A2 - Engelen, Marc
A2 - das Neves Ferreira, Ana Cristina Leal
A2 - Gasperini, Serena
A2 - Groselj, Urh
A2 - Grünert, Sarah C.
A2 - François-Guillaume, Debray
A2 - Guimas, Arlindo
A2 - Gumus, Evren
A2 - Grønborg, Sabine Weller
A2 - Hennermann, Julia B.
A2 - Heras, Javier de las
A2 - Huidekoper, Hidde H.
A2 - Janssen, Mirian Ch
A2 - Ješina, Pavel
A2 - Kölker, Stefan
A2 - Hoytema van Konijnenburg, Eva M.M.
A2 - La Rosa, Alessandro
A2 - Lajic, Svetlana
A2 - Lapatto, Risto
A2 - Leão-Teles, Elisa
A2 - Leuzzi, Vincenzo
A2 - Macário, Maria Carmo
A2 - Magner, Martin
A2 - Marchi, Giacomo
A2 - Martinelli, Diego
A2 - Martins, Esmeralda
A2 - Melone, Mariarosa Anna Beatrice
A2 - Moeslinger, Dorothea
A2 - Monavari, Ahmad Ardeshir
A2 - Moreira, Sónia
A2 - Muschol, Nicole
A2 - Oberg, Andreas
A2 - Opladen, Thomas
A2 - Õunap, Katrin
A2 - Panis, Bianca
A2 - Pierre, Germaine
A2 - Porta, Francesco
A2 - Quijada-Fraile, Pilar
A2 - Ramadža, Danijela Petković
A2 - Rodrigues, Esmeralda
A2 - Rossi, Alessandro
A2 - Sánchez-Pintos, Paula
A2 - Schiaffino, Maria Cristina
A2 - Schumann, Anke
A2 - Stanescu, Sinziana
A2 - Tanšek, Mojca Žerjav
A2 - Taybert, Joanna
A2 - Tazmini, Kiarash
A2 - Tumiene, Birute
A2 - Vanlander, Arnaud
A2 - Verloo, Patrick
A2 - Veroniki, Komninaka
A2 - Verrecchia, Elena
A2 - Weinhold, Natalie
A2 - Žigman, Tamara
A2 - Ørngreen, Mette Cathrine
N1 - Publisher Copyright:
© 2025 The Author(s). Journal of Inherited Metabolic Disease published by John Wiley & Sons Ltd on behalf of SSIEM.
PY - 2025/11
Y1 - 2025/11
N2 - Palliative care should be an integral part of follow-up for patients with life-limiting/life-threatening conditions, irrespective of age and diagnosis. Many patients with inherited metabolic disorders (IMD) have palliative care needs due to multi-systemic conditions without curative treatment options. To map the organisation and accessibility of palliative care across European IMD expert centres, and to explore the experiences of IMD physicians with palliative care, the European Reference Network for Hereditary Metabolic Disorders (MetabERN) invited physicians from all 103 member institutions to participate in a survey covering various aspects of palliative care. Ninety-two physicians from 63 institutions in 23 countries participated. A national plan or strategy for palliative care had been established in most countries (87%). Both children (91%) and adults (89%) had access to palliative care services. Most paediatric (86%) and many adult IMD physicians (67%) used advance care planning. A total of 284 referrals to palliative care were reported, mostly IMD patients with lysosomal and mitochondrial disorders, and neurological, respiratory, cognitive and gastrointestinal comorbidities. However, during the past 5 years, the majority of physicians (60%) had referred 20% or fewer of their deceased patients to palliative care. Although palliative care is available in most European IMD expert centres, only a small proportion of deceased IMD patients has been referred. The findings of this study indicate both a misconception and underutilisation of modern palliative care services. Addressing existing barriers is essential, and both IMD physicians and patients may need more information about available palliative care services and up-to-date indications for referral.
AB - Palliative care should be an integral part of follow-up for patients with life-limiting/life-threatening conditions, irrespective of age and diagnosis. Many patients with inherited metabolic disorders (IMD) have palliative care needs due to multi-systemic conditions without curative treatment options. To map the organisation and accessibility of palliative care across European IMD expert centres, and to explore the experiences of IMD physicians with palliative care, the European Reference Network for Hereditary Metabolic Disorders (MetabERN) invited physicians from all 103 member institutions to participate in a survey covering various aspects of palliative care. Ninety-two physicians from 63 institutions in 23 countries participated. A national plan or strategy for palliative care had been established in most countries (87%). Both children (91%) and adults (89%) had access to palliative care services. Most paediatric (86%) and many adult IMD physicians (67%) used advance care planning. A total of 284 referrals to palliative care were reported, mostly IMD patients with lysosomal and mitochondrial disorders, and neurological, respiratory, cognitive and gastrointestinal comorbidities. However, during the past 5 years, the majority of physicians (60%) had referred 20% or fewer of their deceased patients to palliative care. Although palliative care is available in most European IMD expert centres, only a small proportion of deceased IMD patients has been referred. The findings of this study indicate both a misconception and underutilisation of modern palliative care services. Addressing existing barriers is essential, and both IMD physicians and patients may need more information about available palliative care services and up-to-date indications for referral.
UR - https://www.scopus.com/pages/publications/105019999360
U2 - 10.1002/jimd.70095
DO - 10.1002/jimd.70095
M3 - Article
C2 - 41137497
AN - SCOPUS:105019999360
SN - 0141-8955
VL - 48
JO - Journal of Inherited Metabolic Disease
JF - Journal of Inherited Metabolic Disease
IS - 6
M1 - e70095
ER -